Inherited Cardiac Muscle Disorders: Left Ventricular Noncompaction

Marangou, James, Frenneaux, Michael and Dwivedi, Girish (2018) Inherited Cardiac Muscle Disorders: Left Ventricular Noncompaction. In: Cardiovascular Genetics and Genomics. Springer International Publishing AG, pp. 389-412. ISBN 978-3-319-66112-4

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Abstract

Left ventricular noncompaction (LVNC) is a type of structural cardiac abnormality that displays genotypic and phenotypic heterogeneity. Morphologically, it is characterized by prominent ventricular trabeculae and deep intertrabecular recesses. It has traditionally been thought to be related to intrauterine arrest of myocardial development. While it is classified as a primary cardiomyopathy of genetic origin by the American Heart Association, the European Society of Cardiology classification defines it as an unclassified cardiomyopathy. Originally thought to be a rare disease seen mainly in children, there has been increasing identification in adults likely due to increased awareness and advances in cardiovascular imaging. Furthermore, although it is often associated with other congenital cardiac anomalies it can also be seen in association with dilated, hypertrophic and restrictive cardiomyopathies and in the absence of any cardiac defects.

Item Type: Book Section
Faculty \ School: Faculty of Medicine and Health Sciences > Norwich Medical School
Related URLs:
Depositing User: Pure Connector
Date Deposited: 11 May 2018 15:30
Last Modified: 22 Apr 2020 11:15
URI: https://ueaeprints.uea.ac.uk/id/eprint/67041
DOI: 10.1007/978-3-319-66114-8_12

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