Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) in clinical practice

Li, Ka Hou Christien, Bazoukis, George, Liu, Tong, Li, Guangping, Wu, William KK, Wong, Sunny Hei, Wong, Wing Tak, Chan, Yat Sun, Wassilew, Katharina, Vassiliou, Vassilios S and Tse, Gary (2018) Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) in clinical practice. Journal of Arrhythmia, 34 (1). 11–22. ISSN 1880-4276

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Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is an inherited myocardial disease characterized by fibro-fatty replacement of the right ventricular myocardium, and associated with paroxysmal ventricular arrhythmias and sudden cardiac death (SCD). It is currently the second most common cause of SCD after hypertrophic cardiomyopathy in young people <35 years of age, causing up to 20% of deaths in this patient population. This condition has a male preponderance and is more commonly found in individuals of Italian and Greek descent. To date, there is no single diagnostic test for ARVC/D and the diagnosis is made based on clinical, electrocardiographic, and radiological findings according to the Revised 2010 Task Force Criteria. In this review, we will discuss the mainstay treatment which includes pharmacotherapy, implantable cardioverter-defibrillator insertion for abortion of sudden cardiac death, and in the advanced stages of the disease cardiac transplantation.

Item Type: Article
Uncontrolled Keywords: arrhythmogenic right ventricular cardiomyopathy,arrhythmogenic right ventricular dysplasia
Faculty \ School: Faculty of Medicine and Health Sciences > Norwich Medical School
Depositing User: Pure Connector
Date Deposited: 08 Dec 2017 07:41
Last Modified: 11 Jun 2020 00:41
URI: https://ueaeprints.uea.ac.uk/id/eprint/65710
DOI: 10.1002/joa3.12021

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